Journal of Comprehensive Pediatrics

Published by: Kowsar

Primary Pulmonary Hypertension and Moyamoya Disease: Case Presentation and Review of Literature

Fatemeh Vaziri 1 , Shahla Roodpeyma 1 , * and Narges Ashrafinia 1
Authors Information
1 Department of Pediatric Cardiology, Shahid Modarres Hospital, Shahid Beheshti University of Medical Sciences, Tehran, IR Iran
Article information
  • Journal of Comprehensive Pediatrics: August 10, 2013, 4 (3); 155-9
  • Published Online: June 1, 2013
  • Article Type: Case Report
  • Received: March 13, 2013
  • Accepted: June 9, 2013
  • DOI: 10.17795/compreped-11143

To Cite: Vaziri F, Roodpeyma S, Ashrafinia N. Primary Pulmonary Hypertension and Moyamoya Disease: Case Presentation and Review of Literature, J Compr Ped. 2013 ; 4(3):155-9. doi: 10.17795/compreped-11143.

Copyright © 2013, Iranian Society of Pediatrics. This is an open-access article distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 International License ( which permits copy and redistribute the material just in noncommercial usages, provided the original work is properly cited.
1. Introduction
2. Case Presentation
3. Discussion
  • 1. Galie N, Hoeper MM, Humbert M, Torbicki A, Vachiery JL, Barbera JA, et al. Guidelines for the diagnosis and treatment of pulmonary hypertension. Eur Respir J. 2009; 34(6): 1219-63[DOI][PubMed]
  • 2. Bernstein D. Nelson textbook of pediatrics. 2011; : 1600-1601
  • 3. Sztrymf B, Yaici A, Jais X, Sitbon O, Simonneau G, Humbert M. Idiopathic pulmonary hypertension: what did we learn from genes? Sarcoidosis Vasc Diffuse Lung Dis. 2005; 22 Suppl 1-100[PubMed]
  • 4. Krishnan U. Diagnosis and management of primary pulmonary hypertension. Indian J Pediatr. 2000; 67(3 Suppl)-5[PubMed]
  • 5. Currie S, Raghavan A, Batty R, Connolly DJ, Griffiths PD. Childhood moyamoya disease and moyamoya syndrome: a pictorial review. Pediatr Neurol. 2011; 44(6): 401-13[DOI][PubMed]
  • 6. de Vries RR, Nikkels PG, van der Laag J, Broere G, Braun KP. Moyamoya and extracranial vascular involvement: fibromuscular dysplasia? A report of two children. Neuropediatrics. 2003; 34(6): 318-21[DOI][PubMed]
  • 7. Berger RM, Beghetti M, Humpl T, Raskob GE, Ivy DD, Jing ZC, et al. Clinical features of paediatric pulmonary hypertension: a registry study. Lancet. 2012; 379(9815): 537-46[DOI][PubMed]
  • 8. Calderon Colmenero J, Rylaarsdam M, Camacho L, Attie F, Zabal C, Buendia A. [Primary pulmonary arterial hypertension in children under 2 years of age]. Arch Inst Cardiol Mex. 1991; 61(6): 533-7[PubMed]
  • 9. Hoeper MM, Galie N, Murali S, Olschewski H, Rubenfire M, Robbins IM, et al. Outcome after cardiopulmonary resuscitation in patients with pulmonary arterial hypertension. Am J Respir Crit Care Med. 2002; 165(3): 341-4[DOI][PubMed]
  • 10. Kim YO, Joo SP, Seo BR, Rho YI, Yoon W, Woo YJ. Early clinical characteristics according to developmental stage in children with definite moyamoya disease. Brain Dev. 2013; 35(6): 569-74[DOI][PubMed]
  • 11. Kapusta L, Daniels O, Renier WO. Moya-Moya syndrome and primary pulmonary hypertension in childhood. Neuropediatrics. 1990; 21(3): 162-3[DOI][PubMed]
  • 12. Ou P, Dupont P, Bonnet D. Fibromuscular dysplasia as the substrate for systemic and pulmonary hypertension in the setting of Moya-Moya disease. Cardiol Young. 2006; 16(5): 495-7[DOI][PubMed]
  • 13. Klein A, Fasnacht M, Huisman TA, Neuhaus TJ, Martin E, Boltshauser E. Siblings with infantile cerebral stroke and delayed multivessel involvement--a new hereditary vasculopathy? Eur J Paediatr Neurol. 2007; 11(5): 292-6[DOI][PubMed]
  • 14. Day RW, Brockmeyer DL, Feola GP. Safe treatment of pulmonary hypertension with bosentan in a patient with moyamoya disease and cerebral ischemia. J Child Neurol. 2010; 25(4): 504-7[DOI][PubMed]
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